一位47歲的女性,近三年來有輕度口渴、掉髮、冬天手指頭會變白及變紫。另外,在手掌及手背有明顯的微血管擴張(telangiectasis)。近半年有吞嚥障礙。經抽血檢查發現ANA 1:160 centromere pattern,C3 108 mg/dL,C4 23.5 mg/dL,anti-Scl-70 85 AU/mL(normal<120 AU/mL),anti-centromere protein 218 AU/mL(normal<120 AU/mL),anti-SSA 128 AU/mL(normal<120 AU/mL),anti-dsDNA 108 IU/mL(normal<120 IU/mL),anti-Sm/anti-RNP均為正常。最有可能的診斷為何?
Apolymyositis
BCREST syndrome正確答案
CSjögren's syndrome
Dsystemic lupus erythematosus
答案與詳解
